FBLN5

Fibulin 5 Q9UBX5 FBLN5_HUMAN
Protein Coding Chr 14 14q32.12 Swiss-Prot reviewed Entrez 10516
Mutations
572
CL 70 · Tissue 488
Samples
286
CL 49 · Tissue 230
Peptides
217
unique mutant peptides
Transcripts
3
isoforms mutated

Stats by Source

Total, split by cell line (COSMIC CL / DepMap / PubMed) vs tissue (COSMIC primary tissue)

How the counts split by source
Stats by Source

Total = all mutations for this gene across every source.

Cell line = COSMIC Cell Lines Project + DepMap + PubMed.

Tissue = COSMIC primary-tissue (patient tumour) samples.

Total can exceed cell line + tissue: COSMIC tissue-derived models sit only in global, and a peptide can be shared across both.

TotalCell lineTissue
Mutations57270488
Samples28649230
Peptides21736187

Function

FBLN5 · Fibulin 5

The protein encoded by this gene is a secreted, extracellular matrix protein containing an Arg-Gly-Asp (RGD) motif and calcium-binding EGF-like domains. It promotes adhesion of endothelial cells through interaction of integrins and the RGD motif. It is prominently expressed in developing arteries but less so in adult vessels. However, its expression is reinduced in balloon-injured vessels and atherosclerotic lesions, notably in intimal vascular smooth muscle cells and endothelial cells. Therefore, the protein encoded by this gene may play a role in vascular development and remodeling. Defects in this gene are a cause of autosomal dominant cutis laxa, autosomal recessive cutis laxa type I (CL type I), and age-related macular degeneration type 3 (ARMD3). [provided by RefSeq, Jul 2008].

Isoforms & Proteins

3 transcripts · UniProt mapping is sequence-verified (AA-safe)

About the isoform mapping
Isoforms & Proteins

Each Ensembl transcript (ENST) this gene is mutated on, with its matched UniProt accession.

The mapping is sequence-verified: the UniProt sequence is identical to the transcript translation, so amino-acid positions line up exactly. A * marks an unreviewed (TrEMBL) entry.

Counts are mutations and unique mutant peptides on each transcript.

TranscriptUniProtMutationsPeptides
ENST00000342058 Q9UBX5 294 199
ENST00000267620 G3XA98* 262 184
ENST00000556154 G3V4U0* 16 12

Gene Properties

Type
Protein Coding
Chromosome
14
Cytoband
14q32.12
Entrez ID
Aliases
ADCL2ARCL1AARMD3CMT1HDANCEEVEC

Recurrent Mutations

All 198 amino-acid changes on canonical ENST00000342058 · needle height = samples · drag the mini-map to zoom

What this lollipop shows
Recurrent Mutations

A lollipop / needle plot – the standard way to show recurrent mutations along a protein (as used by cBioPortal and MutationMapper).

X-axis = amino-acid position in the protein.

Needle height & head size = how often that exact amino-acid change was observed (its recurrence). Tall/large heads are mutational hotspots.

The most recurrent changes are labelled; hover any needle for the change, position and counts.

Mutation frequency across cancer types

% of samples with a missense/complex mutation in FBLN5 · cell line vs tissue

How this frequency is counted
Cancer-type mutation frequency

For each cancer type, the fraction of samples that carry at least one missense/complex mutation anywhere in FBLN5 – counted as distinct samples (a sample counts once no matter how many mutations it has).

Split into cell line and tissue; each cell shows mutated / total and the percentage. Cohorts with <20 samples are omitted. Ordered by combined frequency.

Cancer typeCell linesTissue samples
T-Cell Non-Hodgkins Lymphoma
1/26 4%
0/0 0%
Melanoma
12/210 6%
60/1899 3%
T-Lymphoblastic Leukemia
1/40 2%
0/0 0%
Endometrial Carcinoma
3/42 7%
13/612 2%
Other Solid Cancers
1/94 1%
16/1515 1%
Squamous Cell Lung Carcinoma
1/57 2%
8/810 1%
Gastric Carcinoma
1/74 1%
17/1809 1%
Osteosarcoma
2/45 4%
0/166 0%
Non-Small Cell Lung Carcinoma
7/304 2%
7/1390 0%
Hodgkins Lymphoma
0/16 0%
1/122 1%
Ovarian Carcinoma
1/109 1%
7/998 1%
Colorectal Carcinoma
5/143 4%
19/3239 1%
Hepatocellular Carcinoma
0/46 0%
15/2210 1%
Head and Neck Carcinoma
0/85 0%
9/1574 1%
Small Cell Lung Carcinoma
0/9 0%
4/752 1%
Other Sarcomas
0/69 0%
4/699 1%
Bladder Carcinoma
1/58 2%
4/956 0%
Esophageal Squamous Cell Carcinoma
1/51 2%
11/2550 0%
Mesothelioma
0/62 0%
1/165 1%
Cervical Carcinoma
0/35 0%
2/422 0%
Neuroendocrine Tumour
0/154 0%
3/577 1%
Breast Carcinoma
4/144 3%
9/3264 0%
Thyroid Gland Carcinoma
0/45 0%
5/1592 0%
Esophageal Carcinoma
0/23 0%
2/769 0%
Prostate Carcinoma
0/13 0%
5/2105 0%
Glioma
0/52 0%
5/2127 0%
Non-Cancerous
2/104 2%
0/830 0%
Kidney Carcinoma
1/85 1%
3/1862 0%
Pancreatic Carcinoma
0/89 0%
2/1611 0%
B-Cell Non-Hodgkins Lymphoma
0/88 0%
3/2534 0%

Mutation Distribution

Where FBLN5 is mutated · all tissues, split by cell line vs tissue

Mutation counts by tissue
Mutation Distribution

How many mutations in FBLN5 were found in each tissue, across the whole database.

Each bar is a tissue (cell-line and tissue names are merged to the standard tissue), split into cell line and tissue (patient tumour) contributions.

This shows the cancer-context where this gene is recurrently altered.

GTEx Expression

Median TPM across 54 healthy tissues

GTEx Portal ↗
About the expression data
GTEx Expression

Median gene expression (TPM) in normal, non-cancer human tissues from the GTEx project.

Useful for judging tumour specificity – a strong neoantigen target ideally comes from a gene with low expression in healthy tissues.

Scroll or drag the mini-axis below the chart to browse all tissues.

Mutations

All 572 mutations in FBLN5

About the mutation list
Mutations

Every mutation record for this gene, across all samples and sources.

The Sample column links to the cell line (cell-line samples) or the tissue type (tissue samples).

Use the Type / Source filters, the search box, and column sorting to explore; each CAN-IMMUNE ID opens the full mutation & peptide view.

IDSampleTranscriptAA Change CDSTypeSourceMutant PeptideWild-type Peptide