HADHB

Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta P55084 ECHB_HUMAN
Protein Coding Chr 2 2p23.3 Swiss-Prot reviewed Entrez 3032
Mutations
740
CL 84 · Tissue 655
Samples
220
CL 42 · Tissue 177
Peptides
181
unique mutant peptides
Transcripts
4
isoforms mutated

Stats by Source

Total, split by cell line (COSMIC CL / DepMap / PubMed) vs tissue (COSMIC primary tissue)

How the counts split by source
Stats by Source

Total = all mutations for this gene across every source.

Cell line = COSMIC Cell Lines Project + DepMap + PubMed.

Tissue = COSMIC primary-tissue (patient tumour) samples.

Total can exceed cell line + tissue: COSMIC tissue-derived models sit only in global, and a peptide can be shared across both.

TotalCell lineTissue
Mutations74084655
Samples22042177
Peptides18127161

Function

HADHB · Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta

This gene encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the beta subunit catalyzing the 3-ketoacyl-CoA thiolase activity. The encoded protein can also bind RNA and decreases the stability of some mRNAs. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. Mutations in this gene result in trifunctional protein deficiency. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2013].

Isoforms & Proteins

4 transcripts · UniProt mapping is sequence-verified (AA-safe)

About the isoform mapping
Isoforms & Proteins

Each Ensembl transcript (ENST) this gene is mutated on, with its matched UniProt accession.

The mapping is sequence-verified: the UniProt sequence is identical to the transcript translation, so amino-acid positions line up exactly. A * marks an unreviewed (TrEMBL) entry.

Counts are mutations and unique mutant peptides on each transcript.

TranscriptUniProtMutationsPeptides
ENST00000317799 P55084 225 156
ENST00000537713 F5GZQ3* 189 141
ENST00000545822 P55084-2 179 134
ENST00000405867 B5MD38* 147 112

Gene Properties

Type
Protein Coding
Chromosome
2
Cytoband
2p23.3
Entrez ID
Aliases
ECHBMSTP029MTPBMTPDMTPD2TP-BETA

Recurrent Mutations

All 156 amino-acid changes on canonical ENST00000317799 · needle height = samples · drag the mini-map to zoom

What this lollipop shows
Recurrent Mutations

A lollipop / needle plot – the standard way to show recurrent mutations along a protein (as used by cBioPortal and MutationMapper).

X-axis = amino-acid position in the protein.

Needle height & head size = how often that exact amino-acid change was observed (its recurrence). Tall/large heads are mutational hotspots.

The most recurrent changes are labelled; hover any needle for the change, position and counts.

Mutation frequency across cancer types

% of samples with a missense/complex mutation in HADHB · cell line vs tissue

How this frequency is counted
Cancer-type mutation frequency

For each cancer type, the fraction of samples that carry at least one missense/complex mutation anywhere in HADHB – counted as distinct samples (a sample counts once no matter how many mutations it has).

Split into cell line and tissue; each cell shows mutated / total and the percentage. Cohorts with <20 samples are omitted. Ordered by combined frequency.

Cancer typeCell linesTissue samples
T-Lymphoblastic Leukemia
2/40 5%
0/0 0%
Acute Myeloid Leukemia
4/90 4%
0/0 0%
Endometrial Carcinoma
4/42 10%
12/612 2%
Glioblastoma
2/98 2%
0/0 0%
Colorectal Carcinoma
9/143 6%
29/3239 1%
Melanoma
5/210 2%
18/1899 1%
Germ Cell Tumour
1/25 4%
1/169 1%
Other Solid Cancers
2/94 2%
9/1515 1%
Thyroid Gland Carcinoma
0/45 0%
11/1592 1%
Kidney Carcinoma
1/85 1%
12/1862 1%
Non-Small Cell Lung Carcinoma
0/304 0%
11/1390 1%
Gastric Carcinoma
0/74 0%
11/1809 1%
Hepatocellular Carcinoma
2/46 4%
9/2210 0%
Bladder Carcinoma
0/58 0%
5/956 1%
Squamous Cell Lung Carcinoma
1/57 2%
3/810 0%
Esophageal Squamous Cell Carcinoma
0/51 0%
11/2550 0%
Head and Neck Carcinoma
2/85 2%
5/1574 0%
Meningioma
1/3 33%
0/252 0%
Breast Carcinoma
3/144 2%
9/3264 0%
Small Cell Lung Carcinoma
0/9 0%
2/752 0%
Glioma
0/52 0%
5/2127 0%
Biliary Tract Carcinoma
0/54 0%
2/950 0%
Ovarian Carcinoma
0/109 0%
2/998 0%
B-Cell Non-Hodgkins Lymphoma
2/88 2%
2/2534 0%
Esophageal Carcinoma
0/23 0%
1/769 0%
Other Sarcomas
0/69 0%
1/699 0%
Pancreatic Carcinoma
0/89 0%
2/1611 0%
Non-Cancerous
0/104 0%
1/830 0%
Prostate Carcinoma
0/13 0%
2/2105 0%
Neuroblastoma
0/87 0%
1/1331 0%

Mutation Distribution

Where HADHB is mutated · all tissues, split by cell line vs tissue

Mutation counts by tissue
Mutation Distribution

How many mutations in HADHB were found in each tissue, across the whole database.

Each bar is a tissue (cell-line and tissue names are merged to the standard tissue), split into cell line and tissue (patient tumour) contributions.

This shows the cancer-context where this gene is recurrently altered.

GTEx Expression

Median TPM across 54 healthy tissues

GTEx Portal ↗
About the expression data
GTEx Expression

Median gene expression (TPM) in normal, non-cancer human tissues from the GTEx project.

Useful for judging tumour specificity – a strong neoantigen target ideally comes from a gene with low expression in healthy tissues.

Scroll or drag the mini-axis below the chart to browse all tissues.

Mutations

All 740 mutations in HADHB

About the mutation list
Mutations

Every mutation record for this gene, across all samples and sources.

The Sample column links to the cell line (cell-line samples) or the tissue type (tissue samples).

Use the Type / Source filters, the search box, and column sorting to explore; each CAN-IMMUNE ID opens the full mutation & peptide view.

IDSampleTranscriptAA Change CDSTypeSourceMutant PeptideWild-type Peptide