PKHD1

PKHD1 ciliary IPT domain containing fibrocystin/polyductin P08F94 PKHD1_HUMAN
Protein Coding Chr 6 6p12.3-p12.2 Swiss-Prot reviewed Entrez 5314
Mutations
5,250
CL 833 · Tissue 4,348
Samples
2,327
CL 455 · Tissue 1,839
Peptides
2,072
unique mutant peptides
Transcripts
2
isoforms mutated

Stats by Source

Total, split by cell line (COSMIC CL / DepMap / PubMed) vs tissue (COSMIC primary tissue)

How the counts split by source
Stats by Source

Total = all mutations for this gene across every source.

Cell line = COSMIC Cell Lines Project + DepMap + PubMed.

Tissue = COSMIC primary-tissue (patient tumour) samples.

Total can exceed cell line + tissue: COSMIC tissue-derived models sit only in global, and a peptide can be shared across both.

TotalCell lineTissue
Mutations5,2508334,348
Samples2,3274551,839
Peptides2,0723511,763

Function

PKHD1 · PKHD1 ciliary IPT domain containing fibrocystin/polyductin

The protein encoded by this gene is predicted to have a single transmembrane (TM)-spanning domain and multiple copies of an immunoglobulin-like plexin-transcription-factor domain. Alternative splicing results in two transcript variants encoding different isoforms. Other alternatively spliced transcripts have been described, but the full length sequences have not been determined. Several of these transcripts are predicted to encode truncated products which lack the TM and may be secreted. Mutations in this gene cause autosomal recessive polycystic kidney disease, also known as polycystic kidney and hepatic disease-1. [provided by RefSeq, Jul 2008].

Isoforms & Proteins

2 transcripts · UniProt mapping is sequence-verified (AA-safe)

About the isoform mapping
Isoforms & Proteins

Each Ensembl transcript (ENST) this gene is mutated on, with its matched UniProt accession.

The mapping is sequence-verified: the UniProt sequence is identical to the transcript translation, so amino-acid positions line up exactly. A * marks an unreviewed (TrEMBL) entry.

Counts are mutations and unique mutant peptides on each transcript.

TranscriptUniProtMutationsPeptides
ENST00000371117 P08F94 2,989 2,064
ENST00000340994 P08F94-2 2,261 1,663

Gene Properties

Type
Protein Coding
Chromosome
6
Cytoband
6p12.3-p12.2
Entrez ID
Aliases
ARPKDFCYTFPCPCYTPKD4TIGM1

Recurrent Mutations

All 2064 amino-acid changes on canonical ENST00000371117 · needle height = samples · drag the mini-map to zoom

What this lollipop shows
Recurrent Mutations

A lollipop / needle plot – the standard way to show recurrent mutations along a protein (as used by cBioPortal and MutationMapper).

X-axis = amino-acid position in the protein.

Needle height & head size = how often that exact amino-acid change was observed (its recurrence). Tall/large heads are mutational hotspots.

The most recurrent changes are labelled; hover any needle for the change, position and counts.

Mutation frequency across cancer types

% of samples with a missense/complex mutation in PKHD1 · cell line vs tissue

How this frequency is counted
Cancer-type mutation frequency

For each cancer type, the fraction of samples that carry at least one missense/complex mutation anywhere in PKHD1 – counted as distinct samples (a sample counts once no matter how many mutations it has).

Split into cell line and tissue; each cell shows mutated / total and the percentage. Cohorts with <20 samples are omitted. Ordered by combined frequency.

Cancer typeCell linesTissue samples
T-Lymphoblastic Leukemia
9/40 22%
0/0 0%
Glioblastoma
18/98 18%
0/0 0%
Acute Myeloid Leukemia
15/90 17%
0/0 0%
Chronic Myelogenous Leukemia
4/25 16%
0/0 0%
Squamous Cell Lung Carcinoma
10/57 18%
107/810 13%
Melanoma
39/210 19%
235/1899 12%
Non-Small Cell Lung Carcinoma
77/304 25%
128/1390 9%
Endometrial Carcinoma
8/42 19%
68/612 11%
Other Solid Cancers
13/94 14%
129/1515 9%
Hodgkins Lymphoma
8/16 50%
3/122 2%
T-Cell Non-Hodgkins Lymphoma
2/26 8%
0/0 0%
Colorectal Carcinoma
39/143 27%
215/3239 7%
Small Cell Lung Carcinoma
1/9 11%
55/752 7%
Gastric Carcinoma
9/74 12%
114/1809 6%
Bladder Carcinoma
2/58 3%
54/956 6%
Gastrointestinal Stromal Tumour
0/0 0%
7/133 5%
Neuroendocrine Tumour
20/154 13%
16/577 3%
Osteosarcoma
7/45 16%
3/166 2%
Mesothelioma
8/62 13%
2/165 1%
Cervical Carcinoma
3/35 9%
17/422 4%
Adrenocortical Carcinoma
2/3 67%
3/112 3%
Ovarian Carcinoma
17/109 16%
31/998 3%
Esophageal Squamous Cell Carcinoma
11/51 22%
101/2550 4%
Esophageal Carcinoma
1/23 4%
30/769 4%
Head and Neck Carcinoma
9/85 11%
52/1574 3%
Biliary Tract Carcinoma
2/54 4%
34/950 4%
Glioma
7/52 13%
69/2127 3%
Other Sarcomas
4/69 6%
22/699 3%
Chondrosarcoma
2/14 14%
1/75 1%
Hepatocellular Carcinoma
6/46 13%
66/2210 3%

Mutation Distribution

Where PKHD1 is mutated · all tissues, split by cell line vs tissue

Mutation counts by tissue
Mutation Distribution

How many mutations in PKHD1 were found in each tissue, across the whole database.

Each bar is a tissue (cell-line and tissue names are merged to the standard tissue), split into cell line and tissue (patient tumour) contributions.

This shows the cancer-context where this gene is recurrently altered.

GTEx Expression

Median TPM across 47 healthy tissues

GTEx Portal ↗
About the expression data
GTEx Expression

Median gene expression (TPM) in normal, non-cancer human tissues from the GTEx project.

Useful for judging tumour specificity – a strong neoantigen target ideally comes from a gene with low expression in healthy tissues.

Scroll or drag the mini-axis below the chart to browse all tissues.

Mutations

All 5,250 mutations in PKHD1

About the mutation list
Mutations

Every mutation record for this gene, across all samples and sources.

The Sample column links to the cell line (cell-line samples) or the tissue type (tissue samples).

Use the Type / Source filters, the search box, and column sorting to explore; each CAN-IMMUNE ID opens the full mutation & peptide view.

IDSampleTranscriptAA Change CDSTypeSourceMutant PeptideWild-type Peptide