PRKAR1A

Protein kinase cAMP-dependent type I regulatory subunit alpha P10644 KAP0_HUMAN
Protein Coding Chr 17 17q24.2 Swiss-Prot reviewed Entrez 5573
Mutations
970
CL 112 · Tissue 848
Samples
183
CL 33 · Tissue 146
Peptides
151
unique mutant peptides
Transcripts
6
isoforms mutated

Stats by Source

Total, split by cell line (COSMIC CL / DepMap / PubMed) vs tissue (COSMIC primary tissue)

How the counts split by source
Stats by Source

Total = all mutations for this gene across every source.

Cell line = COSMIC Cell Lines Project + DepMap + PubMed.

Tissue = COSMIC primary-tissue (patient tumour) samples.

Total can exceed cell line + tissue: COSMIC tissue-derived models sit only in global, and a peptide can be shared across both.

TotalCell lineTissue
Mutations970112848
Samples18333146
Peptides15123131

Function

PRKAR1A · Protein kinase cAMP-dependent type I regulatory subunit alpha

cAMP is a signaling molecule important for a variety of cellular functions. cAMP exerts its effects by activating the cAMP-dependent protein kinase, which transduces the signal through phosphorylation of different target proteins. The inactive kinase holoenzyme is a tetramer composed of two regulatory and two catalytic subunits. cAMP causes the dissociation of the inactive holoenzyme into a dimer of regulatory subunits bound to four cAMP and two free monomeric catalytic subunits. Four different regulatory subunits and three catalytic subunits have been identified in humans. This gene encodes one of the regulatory subunits. This protein was found to be a tissue-specific extinguisher that down-regulates the expression of seven liver genes in hepatoma x fibroblast hybrids. Mutations in this gene cause Carney complex (CNC). This gene can fuse to the RET protooncogene by gene rearrangement and form the thyroid tumor-specific chimeric oncogene known as PTC2. A nonconventional nuclear localization sequence (NLS) has been found for this protein which suggests a role in DNA replication via the protein serving as a nuclear transport protein for the second subunit of the Replication Factor C (RFC40). Several alternatively spliced transcript variants encoding two different isoforms have been observed. [provided by RefSeq, Jan 2013].

Isoforms & Proteins

6 transcripts · UniProt mapping is sequence-verified (AA-safe)

About the isoform mapping
Isoforms & Proteins

Each Ensembl transcript (ENST) this gene is mutated on, with its matched UniProt accession.

The mapping is sequence-verified: the UniProt sequence is identical to the transcript translation, so amino-acid positions line up exactly. A * marks an unreviewed (TrEMBL) entry.

Counts are mutations and unique mutant peptides on each transcript.

TranscriptUniProtMutationsPeptides
ENST00000589228 P10644 184 144
ENST00000358598 P10644 162 133
ENST00000392711 P10644 162 133
ENST00000536854 P10644 162 133
ENST00000586397 P10644 162 133
ENST00000588188 P10644-2 138 107

Gene Properties

Type
Protein Coding
Chromosome
17
Cytoband
17q24.2
Entrez ID
Aliases
ACRDYS1ADOHRCARCNCCNC1PKR1

Recurrent Mutations

All 144 amino-acid changes on canonical ENST00000589228 · needle height = samples · drag the mini-map to zoom

What this lollipop shows
Recurrent Mutations

A lollipop / needle plot – the standard way to show recurrent mutations along a protein (as used by cBioPortal and MutationMapper).

X-axis = amino-acid position in the protein.

Needle height & head size = how often that exact amino-acid change was observed (its recurrence). Tall/large heads are mutational hotspots.

The most recurrent changes are labelled; hover any needle for the change, position and counts.

Mutation frequency across cancer types

% of samples with a missense/complex mutation in PRKAR1A · cell line vs tissue

How this frequency is counted
Cancer-type mutation frequency

For each cancer type, the fraction of samples that carry at least one missense/complex mutation anywhere in PRKAR1A – counted as distinct samples (a sample counts once no matter how many mutations it has).

Split into cell line and tissue; each cell shows mutated / total and the percentage. Cohorts with <20 samples are omitted. Ordered by combined frequency.

Cancer typeCell linesTissue samples
T-Lymphoblastic Leukemia
4/40 10%
0/0 0%
Chronic Myelogenous Leukemia
2/25 8%
0/0 0%
Gastrointestinal Stromal Tumour
0/0 0%
4/133 3%
Endometrial Carcinoma
3/42 7%
11/612 2%
Rhabdomyosarcoma
3/33 9%
0/171 0%
Thyroid Gland Carcinoma
3/45 7%
11/1592 1%
Colorectal Carcinoma
2/143 1%
26/3239 1%
Melanoma
0/210 0%
17/1899 1%
Hodgkins Lymphoma
0/16 0%
1/122 1%
Neuroendocrine Tumour
2/154 1%
3/577 1%
Medulloblastoma
0/0 0%
3/450 1%
Non-Small Cell Lung Carcinoma
4/304 1%
6/1390 0%
Non-Cancerous
2/104 2%
3/830 0%
Gastric Carcinoma
0/74 0%
10/1809 1%
Bladder Carcinoma
0/58 0%
5/956 1%
Cervical Carcinoma
0/35 0%
2/422 0%
Wilms Tumour
0/5 0%
2/474 0%
Squamous Cell Lung Carcinoma
0/57 0%
3/810 0%
Plasma Cell Myeloma
1/44 2%
0/305 0%
Prostate Carcinoma
2/13 15%
4/2105 0%
Kidney Carcinoma
0/85 0%
5/1862 0%
Other Solid Cancers
0/94 0%
4/1515 0%
Head and Neck Carcinoma
0/85 0%
4/1574 0%
Glioma
0/52 0%
5/2127 0%
Biliary Tract Carcinoma
1/54 2%
1/950 0%
Esophageal Squamous Cell Carcinoma
2/51 4%
3/2550 0%
Breast Carcinoma
1/144 1%
5/3264 0%
B-Cell Non-Hodgkins Lymphoma
0/88 0%
4/2534 0%
Esophageal Carcinoma
0/23 0%
1/769 0%
Other Sarcomas
0/69 0%
1/699 0%

Mutation Distribution

Where PRKAR1A is mutated · all tissues, split by cell line vs tissue

Mutation counts by tissue
Mutation Distribution

How many mutations in PRKAR1A were found in each tissue, across the whole database.

Each bar is a tissue (cell-line and tissue names are merged to the standard tissue), split into cell line and tissue (patient tumour) contributions.

This shows the cancer-context where this gene is recurrently altered.

GTEx Expression

Median TPM across 54 healthy tissues

GTEx Portal ↗
About the expression data
GTEx Expression

Median gene expression (TPM) in normal, non-cancer human tissues from the GTEx project.

Useful for judging tumour specificity – a strong neoantigen target ideally comes from a gene with low expression in healthy tissues.

Scroll or drag the mini-axis below the chart to browse all tissues.

Mutations

All 970 mutations in PRKAR1A

About the mutation list
Mutations

Every mutation record for this gene, across all samples and sources.

The Sample column links to the cell line (cell-line samples) or the tissue type (tissue samples).

Use the Type / Source filters, the search box, and column sorting to explore; each CAN-IMMUNE ID opens the full mutation & peptide view.

IDSampleTranscriptAA Change CDSTypeSourceMutant PeptideWild-type Peptide