UFD1

Ubiquitin recognition factor in ER associated degradation 1 Q92890 UFD1_HUMAN
Protein Coding Chr 22 22q11.21 Swiss-Prot reviewed Entrez 7353
Mutations
199
CL 24 · Tissue 168
Samples
108
CL 17 · Tissue 86
Peptides
92
unique mutant peptides
Transcripts
2
isoforms mutated

Stats by Source

Total, split by cell line (COSMIC CL / DepMap / PubMed) vs tissue (COSMIC primary tissue)

How the counts split by source
Stats by Source

Total = all mutations for this gene across every source.

Cell line = COSMIC Cell Lines Project + DepMap + PubMed.

Tissue = COSMIC primary-tissue (patient tumour) samples.

Total can exceed cell line + tissue: COSMIC tissue-derived models sit only in global, and a peptide can be shared across both.

TotalCell lineTissue
Mutations19924168
Samples1081786
Peptides921277

Function

UFD1 · Ubiquitin recognition factor in ER associated degradation 1

The protein encoded by this gene forms a complex with two other proteins, nuclear protein localization-4 and valosin-containing protein, and this complex is necessary for the degradation of ubiquitinated proteins. In addition, this complex controls the disassembly of the mitotic spindle and the formation of a closed nuclear envelope after mitosis. Mutations in this gene have been associated with Catch 22 syndrome as well as cardiac and craniofacial defects. Alternative splicing results in multiple transcript variants encoding different isoforms. A related pseudogene has been identified on chromosome 18. [provided by RefSeq, Jun 2009].

Isoforms & Proteins

2 transcripts · UniProt mapping is sequence-verified (AA-safe)

About the isoform mapping
Isoforms & Proteins

Each Ensembl transcript (ENST) this gene is mutated on, with its matched UniProt accession.

The mapping is sequence-verified: the UniProt sequence is identical to the transcript translation, so amino-acid positions line up exactly. A * marks an unreviewed (TrEMBL) entry.

Counts are mutations and unique mutant peptides on each transcript.

TranscriptUniProtMutationsPeptides
ENST00000263202 Q92890 113 87
ENST00000399523 Q92890-3 86 69

Gene Properties

Type
Protein Coding
Chromosome
22
Cytoband
22q11.21
Entrez ID
Aliases
UFD1L

Recurrent Mutations

All 87 amino-acid changes on canonical ENST00000263202 · needle height = samples · drag the mini-map to zoom

What this lollipop shows
Recurrent Mutations

A lollipop / needle plot – the standard way to show recurrent mutations along a protein (as used by cBioPortal and MutationMapper).

X-axis = amino-acid position in the protein.

Needle height & head size = how often that exact amino-acid change was observed (its recurrence). Tall/large heads are mutational hotspots.

The most recurrent changes are labelled; hover any needle for the change, position and counts.

Mutation frequency across cancer types

% of samples with a missense/complex mutation in UFD1 · cell line vs tissue

How this frequency is counted
Cancer-type mutation frequency

For each cancer type, the fraction of samples that carry at least one missense/complex mutation anywhere in UFD1 – counted as distinct samples (a sample counts once no matter how many mutations it has).

Split into cell line and tissue; each cell shows mutated / total and the percentage. Cohorts with <20 samples are omitted. Ordered by combined frequency.

Cancer typeCell linesTissue samples
Chronic Myelogenous Leukemia
3/25 12%
0/0 0%
Endometrial Carcinoma
4/42 10%
8/612 1%
Adrenocortical Carcinoma
0/3 0%
1/112 1%
Cervical Carcinoma
0/35 0%
3/422 1%
Plasma Cell Myeloma
1/44 2%
1/305 0%
Melanoma
1/210 0%
10/1899 1%
Germ Cell Tumour
0/25 0%
1/169 1%
Non-Small Cell Lung Carcinoma
3/304 1%
5/1390 0%
Gastric Carcinoma
0/74 0%
8/1809 0%
Head and Neck Carcinoma
2/85 2%
4/1574 0%
Colorectal Carcinoma
0/143 0%
12/3239 0%
Other Solid Cancers
0/94 0%
5/1515 0%
Ovarian Carcinoma
1/109 1%
2/998 0%
Small Cell Lung Carcinoma
0/9 0%
2/752 0%
Glioma
0/52 0%
5/2127 0%
Non-Cancerous
0/104 0%
2/830 0%
Bladder Carcinoma
0/58 0%
2/956 0%
Biliary Tract Carcinoma
0/54 0%
2/950 0%
Esophageal Squamous Cell Carcinoma
0/51 0%
5/2550 0%
Other Sarcomas
0/69 0%
1/699 0%
Esophageal Carcinoma
0/23 0%
1/769 0%
Breast Carcinoma
0/144 0%
4/3264 0%
Squamous Cell Lung Carcinoma
1/57 2%
0/810 0%
Thyroid Gland Carcinoma
0/45 0%
2/1592 0%
Hepatocellular Carcinoma
0/46 0%
2/2210 0%
Prostate Carcinoma
0/13 0%
1/2105 0%
Kidney Carcinoma
0/85 0%
1/1862 0%
B-Cell Non-Hodgkins Lymphoma
0/88 0%
1/2534 0%
B-Lymphoblastic Leukemia
1/55 2%
0/2640 0%

Mutation Distribution

Where UFD1 is mutated · all tissues, split by cell line vs tissue

Mutation counts by tissue
Mutation Distribution

How many mutations in UFD1 were found in each tissue, across the whole database.

Each bar is a tissue (cell-line and tissue names are merged to the standard tissue), split into cell line and tissue (patient tumour) contributions.

This shows the cancer-context where this gene is recurrently altered.

Mutations

All 199 mutations in UFD1

About the mutation list
Mutations

Every mutation record for this gene, across all samples and sources.

The Sample column links to the cell line (cell-line samples) or the tissue type (tissue samples).

Use the Type / Source filters, the search box, and column sorting to explore; each CAN-IMMUNE ID opens the full mutation & peptide view.

IDSampleTranscriptAA Change CDSTypeSourceMutant PeptideWild-type Peptide